Multiple Papulonodules over Face and Trunk A Rare Case Report
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Case Report

Multiple Papulonodules over Face and Trunk A Rare Case Report

Turk J Dermatol 2021;15(4):107-112 DOI: 10.4103/tjd.tjd_54_21
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Abstract

Familial cylindromatosis (turban tumor syndrome) is a very rare neoplasm originating from eccrine or apocrine glands. It is an autosomal dominant condition, characterized by multiple cylindromas commonly presenting over face or scalp. We report a case of familial cylindromatosis diagnosed on the basis of clinical, dermoscopic, and histopathological findings in a 70-year-old female. The case is reported due to its rare occurrence in Indian scenario.

Keywords: Dermoscopy, familial cylindromatosis, jigsaw puzzle, turban tumor